Tag Archives | Urea Cycle

Reactions of Urea Cycle | Protein Metabolism

The below mentioned article provides a short note on the Reactions of Urea Cycle. Carbamoyl phosphate is formed by the condensation of one mol of phosphate (derived from ATP) being catalyzed by the enzyme carbamoyl phosphate synthetase which is present in liver mitochondria of all ureotelic organisms including humans. In addition to magnesium ion (Mg++), N-acetyl-glutamate (a dicarboxylic acid) is [...]

By |2016-07-30T17:19:35+00:00July 30, 2016|Protein Metabolism|Comments Off on Reactions of Urea Cycle | Protein Metabolism

Metabolic Disorders in Urea Cycle | Protein Metabolism

The following points highlight the five major metabolic disorders in urea cycle. The disorders are: 1. Hyperammonemia Type I 2. Hyperammonemia Type II 3. Citrullinemia 4. Arginosuccinic Aciduria 5. Hyperargininemia. Urea Cycle: Metabolic Disorder # 1. Hyperammonemia Type I: a. This is a familial disorder. b. This occurs due to the deficiency of the enzyme carbamoyl phosphate synthetase. c. It [...]

By |2016-07-30T17:19:33+00:00July 30, 2016|Protein Metabolism|Comments Off on Metabolic Disorders in Urea Cycle | Protein Metabolism
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